Table 4

Histiocytoses of the R group

Histiocytoses of the R group
Familial RDD
 Faisalabad (or H) syndrome (OMIM #602782)
 FAS deficiency or ALPS-related RDD (OMIM #601859)
 Familial RDD not otherwise specified
Classical (nodal) RDD
 Without IgG4 syndrome
 IgG4 associated
Extranodal RDD
 Bone RDD
 CNS RDD without IgG4 syndrome
 CNS RDD, IgG4 associated
 Single-organ RDD other than lymph node, skin, and CNS, without IgG4 syndrome
 Single-organ RDD other than lymph node, skin, and CNS, IgG4 associated
 Disseminated RDD
Neoplasia-associated RDD
 RDD postleukemia
 RDD postlymphoma
 RDD associated with MH
 RDD associated with LCH or ECD
Immune disease-associated RDD
 SLE related
 IJA related
 AIHA associated
 HIV associated
Other non-C non-L non-M non-H histiocytoses
  • AIHA, autoimmune hemolytic anemia; IJA, idiopathic juvenile arthritis; OMIM, Online Mendelian Inheritance in Man.