Table 1

Histiocytoses of the L group

DiseaseSubtypes
LCHLCH SS
LCH lung+
LCH MS-RO+
LCH MS-RO
Associated with another myeloproliferative/myelodysplastic disorder
ICH
 ECDECD classical type
ECD without bone involvement
Associated with another myeloproliferative/myelodysplastic disorder
Extracutaneous or disseminated JXG with MAPK-activating mutation or ALK translocations
Mixed ECD and LCH
  • ECD, Erdheim-Chester disease; ICH, indeterminate cell histiocytosis; LCH, Langerhans cell histiocytosis; MS, multiple system; RO, risk organ; SS, single system.